Klippel - Trenaunay syndrome (KT syndrome) The triad of KT syndrome is:- Cutaneous vascular malformation —> Most commonly capillary malformation. Bony capillary malformation and soft tissue hypertrophy. Venous abnormalities —> Deep venous system may be absent or hypoplastic. The anomaly present at birth and usually involves lower limb. When there is associated Arterio - venous malformation, it is known as Klippel - Trenaunay - Weber syndrome. Thick walled venous varicocities typically become apparent ipsilateral to the vascular malformation —> May be pulsatile because ofAV malformation.
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