A 6-month-old boy from a consanguineous family in North India presents with bilateral profound sensorineural hearing loss detected on universal newborn hearing screening. Audiometry shows bilateral symmetric hearing thresholds >90 dB across all frequencies. Tympanometry is normal (type A), and MRI of the temporal bones shows normal cochlear anatomy with intact cochlear nerves. Vestibular testing is normal. The clinical and genetic findings are consistent with the condition marked **A** in the diagram — DFNB3 due to MYO15A mutations. Which of the following best describes the primary pathophysiological mechanism underlying this form of hearing loss?
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