A 12-year-old boy from a consanguineous family presents with progressive bilateral sensorineural hearing loss. Audiometry shows the pattern marked **B** in the diagram. On imaging, an enlarged vestibular aqueduct (EVA) is confirmed, and thyroid examination reveals a firm goiter. Genetic testing reveals biallelic mutations in the SLC26A4 gene. Which of the following best describes the pathophysiologic basis of the hearing loss pattern seen at **B**?
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