A 6-year-old girl presents with a short neck, limited cervical spine mobility, and inability to abduct her right eye. Audiometry reveals bilateral severe sensorineural hearing loss. High-resolution temporal bone CT shows a Mondini deformity with enlarged vestibular aqueduct. The hearing loss pattern marked **A** in the diagram is consistent with Wildervanck syndrome. Which of the following best describes the embryological basis and inheritance pattern of this condition?
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