A 3-year-old girl with Rett syndrome presents with progressive developmental regression since 18 months of age, loss of purposeful hand skills, language, and social engagement. She has developed stereotyped hand-wringing movements, seizures, and acquired microcephaly. An EEG is performed. The pattern marked **A** in the diagram—central rhythmic theta with multifocal spikes and slowing during the regression stage—is characteristic of which stage of Rett syndrome?
Ready to test yourself?
Test your Pediatrics knowledge with AI-powered MCQs and detailed explanations — no signup required to try.
Sign up free and practice all 1 Rett Syndrome MECP2 EEG MCQs with AI-powered explanations tailored to your performance.
Create Free Account